Browsing by Author "Kazimi, Mirjalal"
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Article Crigler-Najjar Sendromunda Karaciğer Nakli(2024) Abdullayeva, Madina; Vatansever, Safa; Kazimi, Mirjalal; Beydullayev, Kamran; Asadov, Kanan; Yusifli, Zarifa; Rasulzada, HajıCrigler-Najjar sendromu, unkonjüge hiperbilirubinemiye neden olan nadir, kalıtsal bir hastalıktır. Karaciğer nakli, Crigler-Najjar sendromu için kesin tedavi sağlayan bir seçenektir. Bu olgu sunumunda Crigler-Najjar sendromu nedeniyle karaciğer nakli yapılan iki hasta sunuldu. Gilbert sendromu olarak yanlış teşhis konulan ilk hasta 15 yaşında bir erkekti. Var olan konuşma ve yürüme bozukluğu karaciğer nakli sonrası kısmi olarak düzeldi. İkinci hasta 22 yaşında erkekti. Hastalığın hafif bir klinik formuna sahip olmasına rağmen, karaciğer fibrozisi gelişmişti. Karaciğer nakli her iki hastaya da önemli bir morbidite olmaksızın başarıyla uygulandı.Article Simultaneous Live Donor Liver Transplantation, Aortic Valve Replacement, and Atrial Septal Defect Repair in a Patient With End Stage Liver Disease: a Case Report(Elsevier Science Inc, 2023) Kazimi, Mirjalal; Beydullayev, Kamran; Farajov, Elnur; Shindiyeva, Saida; Jafarova, Shahnaz; Khalilov, Zaur; Nadirov, Tariyel; Dirican, NigarValvular heart disease creates an important barrier for orthotopic liver transplantation in patients with end-stage liver disease and increases mortality. Selection of the appropriate surgical scheme and adequate postoperative management can be lifesaving in these cases. This study presents a 32-year-old man diagnosed with hepatitis C-associated cirrhosis and severe aortic regurgitation due to subacute bacterial endocarditis. Initially, simultaneous aortic valve replacement (AVR) and live donor liver transplantation (LDLT) was planned. However, intraoperative transesopha- geal echocardiography revealed an additional atrial septal defect (ASD) and AVR, ASD repair, and LDLT surgery were performed. During the 2-year follow-up period, there were no early or late complications. To the best of our knowledge, this is the first patient to have simultaneous AVR, ASD repair, and LDLT surgery. Additionally, the present case is also unique in being the first person in the Republic of Azerbaijan to undergo concomitant cardiac surgery and LDLT.

